Laparoscopy and intersex: report of 5 cases of male pseudohermaphroditism.

نویسندگان

  • Mohamed Gad El-Moula
  • Hirofumi Izaki
  • Fathy El-Anany
  • Alaa Abd El-Moneim
  • Abd El-Moneim El-Haggagy
  • Yasser Abdelsalam
  • Ahmad Abolyosr
  • Tomoteru Kishimoto
  • Natsuo Oka
  • Masayuki Takahashi
  • Tomoharu Fukumori
  • Hiro-Omi Kanayama
چکیده

From May, 1999 to August, 2006, we performed laparoscopic diagnosis and treatment for 103 cases of impalpable testes. Among those we found 5 cases of male pseudohermaphroditism of different etiologies. Three males presented by impalpable testes with ambiguous genitalia and 2 females presented by primary amenorrhea. All of them have 46-XY normal male chromosomal pattern. In the first 3 cases, the etiology was complete gonadal dysgenesis, and 2 cases with persistent Mullerian syndrome. Timed gonadectomy for the first case and laparoscopic orchiopexy for the other 2 cases were performed. For the other 2 female cases, the etiology was complete androgen insensitivity syndrome and laparoscopic bilateral orchiectomy was performed for both of them. All the procedures were done without complications with satisfactory results.

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عنوان ژورنال:
  • The journal of medical investigation : JMI

دوره 55 1-2  شماره 

صفحات  -

تاریخ انتشار 2008